Andersons pediatric cardiology 694

Initial manuscript describing what became known as asplenia and now contemporarily is understood to be right isomerism... Manuscript that stresses the importance of how the description o

feeding and growth, infection risks, and long-term complications when inpatient, clinicians should prepare families for successful management of their child at home and in the ambulatory setting.

Ivemark BI Implications of agenesis of the spleen

on the pathogenesis of conotruncus anomalies in childhood; an analysis of the heart

malformations in the splenic agenesis syndrome,

with fourteen new cases Acta Paediatr Suppl.

1955;44:7–110

Initial manuscript describing what became known

as asplenia and now contemporarily is understood to be right isomerism

Van Praagh R, David I, Wright GB, Van Praagh S Large RV plus small LV is not single RV

Circulation 1980;61:1057–1059.

Manuscript that stresses the importance of how the description of cardiac morphology needs to be described in relation to features that are

constant This is a notion of particular importance in isomerism and demonstrates why the atrial appendages should be used as the basis of segregating isomerism

Uemura H, Ho SY, Devine WA, Anderson RH

Analysis of visceral heterotaxy according to splenic status, appendage morphology, or both

Am J Cardiol 1995;76:846–849.

A necroscopy study characterizing the features of

hearts with isomerism, with particular focus on whether splenic status or atrial appendage

morphology is more useful in segregating

isomerism The first study to demonstrate that more defined, homogenous segregation can be achieved based on atrial appendage morphology versus splenic morphology

Uemura H, Ho SY, Devine WA, Kilpatrick LL,

Anderson RH Atrial appendages and venoatrial connections in hearts from patients with visceral

heterotaxy Ann Thorac Surg 1995;60:561–569.

A necroscopy study investigating the venoatrial connections in hearts with isomerism This study defines the superior and inferior caval vein

connections in these hearts as well as the

pulmonary venous connections, highlighting the differences in venoatrial connections between right and left isomerism

Jacobs JP, Anderson RH, Weinberg PM, et al The nomenclature, definition and classification of cardiac structures in the setting of heterotaxy

Cardiol Young 2007;17(suppl 2):1–28.

This is an effort by a large working group

attempting to describe a uniform system by

which to describe so-called heterotaxy, now

understood to be better described as isomerism

Van Praagh R, Van Praagh S Atrial isomerism in